Prosthodontic management of hypohidrotic ectodermal dysplasia: a case report

Emilija Bajraktarova Valjakova; Cvetanka Misevska; Vesna Korunoska Stevkovska; Nikola Gigovski; Ana Sotirovska Ivkovska; Bona Bajraktarova; Ljuben Guguvcevski

doi:10.5937/sejodr2-15244

Emilija Bajraktarova Valjakova Ss. Cyril and Methodius University of Skopje, Faculty of Dentistry, Department of Prosthodontics + PHO University Dental Clinical Centre “St. Pantelejmon”, Department of Prosthodontics
Cvetanka Misevska Ss. Cyril and Methodius University of Skopje, Faculty of Dentistry, Department of Prosthodontics + PHO University Dental Clinical Centre “St. Pantelejmon”, Department of Orthodontics
Vesna Korunoska Stevkovska Ss. Cyril and Methodius University of Skopje, Faculty of Dentistry, Department of Prosthodontics + PHO University Dental Clinical Centre “St. Pantelejmon”, Department of Prosthodontics
Nikola Gigovski Ss. Cyril and Methodius University of Skopje, Faculty of Dentistry, Department of Prosthodontics + PHO University Dental Clinical Centre “St. Pantelejmon”, Department of Prosthodontics
Ana Sotirovska Ivkovska Ss. Cyril and Methodius University of Skopje, Faculty of Dentistry, Department of Prosthodontics + PHO University Dental Clinical Centre “St. Pantelejmon”, Department of Pediatric Dentistry
Bona Bajraktarova Ss. Cyril and Methodius University of Skopje, Faculty of Dentistry, Department of Prosthodontics
Ljuben Guguvcevski Ss. Cyril and Methodius University of Skopje, Faculty of Dentistry, Department of Prosthodontics + PHO University Dental Clinical Centre “St. Pantelejmon”, Department of Prosthodontics

DOI: https://doi.org/10.5937/sejodr2-15244

Abstract

Introduction: Ectodermal dysplasia (ED) is a hereditary disorder associated with developmental disorders of two or more structures of ectodermal embryonic origin. Hypodontia or anodontia of the primary and permanent dentition, poorly developed alveolar ridgesand improper maxillo - mandibular relations, are the most common oral manifestations. Management of patients with ectodermaldysplasia requires a multidisciplinary team approach.

Case presentation: A 6.5 year-old boy with hypohidrotic ectodermal dysplasia (HED) presented in this article, had typical featuresof HED: hypohidrosis, hypotrichosis, severe hypodontia, atrophic alveolar ridges, old-looking facial expression. According to thepatient’s age and clinical findings, removable complete over-denture prosthesis in both arches was the treatment of choice.

Conclusion: In patients with ED, it is important to establish correct maxillo - mandibular relations and normal function of thedento-facial system (chewing, swallowing, and speaking). Prosthodontic treatment has a major impact on aesthetics and functions, facilitates psychological development and improves emotional condition and social life of the patient.

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