Retka primarna intrahepatična litijaza kod mladog bolesnika

  • Milan Jovanović Military Medical Academy, Department of Abdominal Surgery Belgrade, Serbia; University of Defence, Faculty of Medicine of the Military Medical Academy, Belgrade, Serbia
  • Mihailo Bezmarević Military Medical Academy, Department of Abdominal Surgery Belgrade, Serbia; University of Defence, Faculty of Medicine of the Military Medical Academy, Belgrade, Serbia
  • Srdjan Petković Military Medical Academy, Department of Abdominal Surgery, Belgrade, Serbia
  • Boško Milev Military Medical Academy, Department of Abdominal Surgery, Belgrade, Serbia; University of Defence, Faculty of Medicine of the Military Medical Academy, Belgrade, Serbia
  • Miroslav Mitrović Military Medical Academy, Department of Abdominal Surgery, Belgrade, Serbia; University of Defence, Faculty of Medicine of the Military Medical Academy, Belgrade, Serbia
  • Miodrag Jocić University of Defence, Faculty of Medicine of the Military Medical Academy, Belgrade, Serbia; Military Medical Academy, Institute for Transfusiology and Haemobiology, Belgrade, Serbia;
  • Marina Jovanović University of Kragujevac, Faculty of Medical Sciences, Department of Internal Medicine, Kragujevac, Serbia
  • Darko Mirković Military Medical Academy, Department of Abdominal Surgery Belgrade, Serbia; University of Defence, Faculty of Medicine of the Military Medical Academy, Belgrade, Serbia
Ključne reči: žučni putevi, intrahepatički, holedoholitijaza, dijagnoza, hirurgija, operativne procedure, ureteroskopi, lečenje, ishod

Sažetak


Uvod. Intrahepatična litijaza (IHL) je bolest koja se javlja kod osoba srednjeg i starijeg životnog doba. Pojava IHL kod mladih osoba je retka, a diferencijalna dijagnoza uključuje primarni sklerozirajući holangitis, rekurentni piogeni holangitis, defekt transportera žučne kiseline, Karolijevu bolest i druge poznate genetske bolesti. Lečenje je često složeno, sa ciljem da se spreče komplikacije. U ovom radu prikazujemo dijagnozu i lečenje bolesnika mlađeg životnog doba sa IHL korišćenjem fleksibilnog ureteroskopa promera 4 Fr. Prikaz bolesnika. Muškarac star 25 godina, sa ranije poznatom dijagnozom IHL i ponavljajućim napadima bolova u stomaku koji su zahtevali medicinski tretman, javio se na pregled. Magnetna rezonanca abdomena pokazala je segmentnu stenozu levog žučnog kanala i segmentnog žučnog kanala za lateralnu sekciju sa intraduktalnim konkrementima, kao i proksimalnom dilatacijom, te blagu dilataciju žučnih puteva za II i III segment jetre. Tokom operacije urađeni su holangiografija i ultrazvuk jetre. Žučni kanali su isprani kroz holedohotomiju i izvršena je ekstirpacija nekoliko konkremenata. Pregled žučnih puteva urađen je holedoskopom, a preostali konkrementi su uklonjeni fleksibilnim ureteroskopom. Zaključak. Segmentni žučni kanali jetre mogu se eksplorisati bez traume fleksibilnim ureteroskopom. U odabranim slučajevima, kod izolovane litijaze u jednom režnju jetre i odsustva pratećih bolesti, IHL se može lečiti hirurški, bez resekcije jetre. Prikazani slučaj je jedinstven jer nismo uradili resekciju jetre, već ekstrakciju konkremenata iz žučnih kanala, što je bio odgovarajući tretman, imajući u vidu odsustvo recidiva tokom dvogodišnjeg praćenja.

Biografija autora

Miodrag Jocić, University of Defence, Faculty of Medicine of the Military Medical Academy, Belgrade, Serbia; Military Medical Academy, Institute for Transfusiology and Haemobiology, Belgrade, Serbia;

Phone: +38165 2500 550

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Objavljeno
2023/11/30
Rubrika
Prikaz bolesnika