Neobična klinička prezentacija kongenitalnog holesteatoma srednjeg uv

  • Bojana Bukurov Clinic for Otorhinolaryngology and Maxillofacial Surgery, Clinical Center of Serbia, Faculty of Medicine, University of Belgrade, Belgrade, Serbia
  • Borivoj Babić Clinic for Otorhinolaryngology and Maxillofacial Surgery, Clinical Center of Serbia, Faculty of Medicine, University of Belgrade, Belgrade, Serbia
  • Milovan Dimitrijević Clinic for Otorhinolaryngology and Maxillofacial Surgery, Clinical Center of Serbia, Faculty of Medicine, University of Belgrade, Belgrade, Serbia
  • Miljan Folić Clinic for Otorhinolaryngology and Maxillofacial Surgery, Clinical Center of Serbia, Faculty of Medicine, University of Belgrade, Belgrade, Serbia
  • Nenad Arsović Clinic for Otorhinolaryngology and Maxillofacial Surgery, Clinical Center of Serbia, Faculty of Medicine, University of Belgrade, Belgrade, Serbia
Ključne reči: cholesteatoma||, ||holesteatom, congenital abnormalities||, ||anomalije, ear, middle||, ||uvo, srednje, diagnosis||, ||dijagnoza, otorhinolaryngologic surgical procedures||, ||hirurgija, otorinolaringološka, procedure.,

Sažetak


Uvod. Kongenitalni holesteatom lokalizovan u kavumu timpani retko je oboljenje, još uvek nerazjašnjene etiologije. Do sada je objavljeno samo nekoliko radova u medicinskoj literaturi o kongenitalnom holestatomu u ovalnom prozoru sa minimalnom kliničkom prezentacijom. Prikaz bolesnika. Prikazana je 16-godišnja devojčica sa kongenitalnim holesteatomom lokalizovanim u ovalnom prozoru sa minimalnim kliničkim simptomima. Pronađen je mali holesteatom koji je u popunosti ispunjavao fosu ovalis i imitirao otosklerotični proces u kavumu timpani. Operacija je započeta kao stapedotomija, a kada je proces konstatovan, nastavljena je kao mastoidektomija kroz retroaurikularni pristup. Zaključak. Trebalo bi uvek razmotriti dijagnozu kongenitalnog holesteatoma kod dece, čak i kada simptomi imitiraju neko drugo oboljenje srednjeg uva, u našem slučaju otosklerozu.

Biografije autora

Bojana Bukurov, Clinic for Otorhinolaryngology and Maxillofacial Surgery, Clinical Center of Serbia, Faculty of Medicine, University of Belgrade, Belgrade, Serbia
Dr
Borivoj Babić, Clinic for Otorhinolaryngology and Maxillofacial Surgery, Clinical Center of Serbia, Faculty of Medicine, University of Belgrade, Belgrade, Serbia
Prof, Dr sci med, Načelnik Odseka za audiologiju i vestibulologiju
Milovan Dimitrijević, Clinic for Otorhinolaryngology and Maxillofacial Surgery, Clinical Center of Serbia, Faculty of Medicine, University of Belgrade, Belgrade, Serbia
Doc, Dr sci med, Načelnik Dečjeg odeljenja
Miljan Folić, Clinic for Otorhinolaryngology and Maxillofacial Surgery, Clinical Center of Serbia, Faculty of Medicine, University of Belgrade, Belgrade, Serbia
Dr
Nenad Arsović, Clinic for Otorhinolaryngology and Maxillofacial Surgery, Clinical Center of Serbia, Faculty of Medicine, University of Belgrade, Belgrade, Serbia
MD, PhD, Head of Pediatric Otolaringology Department

Reference

Levine JL, Wright CG, Pawlowski KS, Meyerhoff WL. Postnatal persistence of epidermoid rests in the human middle ear. La-ryngoscope 1998; 108(1 Pt 1): 70−3.

Persaud R, Hajioff D, Trinidale A, Khemani S, Battacharya MN, Pa-padimitriou N, et al. Evidence-based review of etiopathogenic theories of congenital and acquired cholesteatoma. J Laryngol Otol 2007; 121(11): 1013−9.

Lim HW, Yoon TH, Kang WS. Congenital cholesteatoma: clini-cal features and growth patterns. Am J Otolaryngol 2012; 33(5): 538−42.

Kojima H, Tanaka Y, Shiwa M, Sukurai Y, Moriyama H. Conge-nital cholesteatoma clinical features and surgical resulats. Am J Otolaryngol 2006; 27(5): 299−305.

McGill TJ, Merchant S, Healy GB, Friedman EM. Congenital cho-lesteatoma of the middle ear in children: a clinical and histopa-thological report. Laryngoscope 1991; 101(6 Pt 1): 606−13.

Wang R, Zubick HH, Vernick DM, Strome M. Bilateral congenital middle ear cholesteatomas. Laryngoscope 1984; 94(11 Pt 1): 1461−3.

Levenson MJ, Michaels L, Parisier SC, Juarbe C. Congenital choles-teatomas in children: an embryologic correlation. Laryngos-cope 1988; 98(9): 949−55.

Iino Y, Imamura Y, Hiraishi M, Yabe T, Suzuki J. Mastoid pneu-matization in children with congenital cholesteatoma: an aspect of the formation of open-type and closed-type cholesteatoma. Laryngoscope 1998; 108(7): 1071−6.

Warren FM, Bennett ML, Wiggins RH 3rd, Saltzman KL, Blevins KS, Shelton C, et al. Congenital cholesteatoma of the mastoid temporal bone. Laryngoscope 2007; 117(8): 1389−94.

Mevio E, Gorini E, Sbrocca M, Artesi L, Lenzi A, Lecce S, et al. Congenital cholesteatoma of mastoid origin. Otolaryngol Head Neck Surg 2002; 127(4): 346−8.

Lee JH, Hong SJ, Park CH, Jung SH. Congenital cholesteatoma of mastoid origin. J Laryngol Otol 2007; 121(11): e20.

Objavljeno
2015/04/23
Broj časopisa
Rubrika
Prikaz bolesnika